Uhl Anomaly as a Maximum Variant of Arrhythmogenic Right Ventricular or Biventricular Cardiomyopathy

Medical Care Unit Cardiology, Elze, Germany

*Corresponding Author: Prof.Dr.med. Stefan Peters, Medical Care Unit Elze, Cardiology, Königsberger Str. 1, 31008 Elze, Germany, Tel: +49 5068 9337022, Email: [email protected]

Received Date: July 31, 2025

Published Date: October 23, 2025

Citation: Peters S. (2025). Uhl Anomaly as a Maximum Variant of Arrhythmogenic Right Ventricular or Biventricular Cardiomyopathy. Mathews J Cardiol. 9(2):41.

Copyrights: Peters S. © (2025).

ABSTRACT

The cause of Uhl anomaly remains unclear. A maximum variant of arrhythmogenic right ventricular or even biventricular cardiomyopathy is possible or a distinct unknown form of origin. Method: The shape of the right ventricle, histology and appearance the ECG findings were analyzed. Results: As a maximum variant of arrhythmogenic right ventricular or biventricular cardiomyopathy the shape of the intraventricular septum turns to a S-shaped form overlapping the left ventricle. In histology, lipomatosis appeared in new-born and early childhood and in later stages turns to pure fibrosis. The ECG of patients are likely to be arrhythmogenic right ventricular or in this single case biventricular cardiomyopathy but without localized right precordial QRS prolongation and terminal activation delay. In later stages complete right bundle branch block is more and more evident. Conclusions: There is evidence that Uhl anomaly might be the maximum variant of aarhythmogenic right ventricular or biventricular cardiomyopathy

Keywords: Uhl Anomaly, Arrhythmogenic Right Ventricular Cardiomyopathy, Low Voltage in Limb Leads, T-Wave Inversions, Fibrosis.